MAXILLOFACIAL RADIOLOGY Nevoid Basal Cell Carcinoma Syndrome


  • Lené Merbold
  • Zarah Yakoob General Management (GIBS Pret), Department of Oral and Maxillofacial Pathology, School of Dentistry, Faculty of Health Sciences, University of Pretoria, South Africa



distal, lesion


An 18-year-old male patient presented at our dental clinic in 2009 for a dental assessment. A panoramic radiograph was taken to evaluate dental crowning (Figure 1). An incidental finding was noted in the right maxilla, presenting as a well-demarcated, round, unilocular, radiolucent lesion with a corticated rim extending from the right maxillary tuberosity area to distal of the 16 causing.
impaction of the 18. A biopsy was taken and diagnosed as an odontogenic keratocyst (OKC) that was subsequently enucleated. In 2021 the patient returned, and another panoramic radiograph (Figure 2) and a Waters view was taken where calcification of the falx cerebri was seen (Figure 3). On the panoramic radiograph an additional mandibular lesion was visible that presented as a well-demarcated, round, unilocular, radiolucent lesion with a corticated rim extending from distal of the 46 into the missing 47, 48 area. A CBCT was then.
taken to further analyse the lesions (Figure 4). A biopsy was taken in the right posterior mandible and diagnosed as an OKC. In 2023 the patient returned and a CBCT was taken. The right maxilla showed increased bone density adjacent to the enucleated lesion (Figure 5).


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How to Cite

Merbold, L., & Yakoob, Z. (2023). MAXILLOFACIAL RADIOLOGY Nevoid Basal Cell Carcinoma Syndrome. South African Dental Journal, 78(07), 338–339.